Immunophenotyping and Protein Profiling of Fontan-associated Plastic Bronchitis Airway Casts
نویسندگان
چکیده
منابع مشابه
Risk Factors and Outcome of Fontan‐Associated Plastic Bronchitis: A Case‐Control Study
BACKGROUND The onset of plastic bronchitis (PB) can be debilitating in survivors of Fontan surgery. The rarity of this complication makes designing studies to understand risk factors for PB challenging. This 2-center case-control study aimed to describe patient outcomes and to assess the association of antecedent patient factors with PB development. METHODS AND RESULTS Using center registries...
متن کاملPharmacotherapy challenges of Fontan-associated plastic bronchitis: a rare pediatric disease.
Pediatric pharmacotherapy is often challenging due to the paucity of available clinical data on the safety and efficacy of drugs that are commonly used in children. This quandary is even more prevalent in children with rare diseases. Although extrapolations for dosing and administration are often made from available adult data with similar disease states, this translation becomes even more prob...
متن کامل[Association of plastic bronchitis to protein-losing enteropathy after fontan operation].
We report an unusual case of association of plastic bronchitis (PB) to protein-losing enteropathy (PLE) in a girl of 4 years and 9 months of age with double inlet single left ventricle and ventriculoarterial concordance. submitted to total cavopulmonary surgery. with an intracardiac lateral tunnel at the age of three. The elimination of the 10 cm fibrin bronchial mold (PB) and the alpha-1-antit...
متن کامل[Plastic bronchitis].
Bronchitis plastica is a rare disorder that can occur at any age. It is characterised by formation of large, branching bronchial casts, which are often expectorated, but may be discovered only by bronchoscopy. In most cases, bronchial casts are secondary to underlying diseases of the lung, heart or lymph vessels. We report a case of plastic bronchitis associated with bilateral chylothorax. Prog...
متن کاملPlastic Bronchitis
Figure 2. Bronchial Cast showing complete casting of right upper lobe (RUL), right middle lobe (RML) and right lower lobe (RLL). Figure 1. Computed tomography of the chest showing consolidation of right lower lobe with arrow showing pulgged bronchioles. A 45-year-old male with a one-month history of dyspnea and cough presented with productive sputum consisting of bronchial casts for several day...
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ژورنال
عنوان ژورنال: Annals of the American Thoracic Society
سال: 2013
ISSN: 2325-6621
DOI: 10.1513/annalsats.201209-080oc